RT期刊文章SR电子T1调查嗅觉损害小脑性共济失调(P05.015)摩根富林明神经病学神经学乔FD Lippincott Williams &威尔金斯SP P05.015 OP P05.015 VO 78是1补充首页A1马里亚纳Moscovich A1雷纳托穆尼奥斯A1赫利奥Teive A1斑鳟属Raskin A1吉林刘A1凯伦·麦克法兰A1 Tetsuo Ashizawa A1 Andrew Lees A1劳拉Silveira-Moriyama年2012 UL //www.ez-admanager.com/content/78/1_Supplement/P05.015.abstract AB目的:探讨小脑性共济失调的嗅觉障碍。背景的主要临床表现脊髓小脑的共济失调(SCA)由于小脑的参与及其连接特性。小脑活动一直观察到在嗅觉功能成像研究,但负责此连接的解剖路径尚未阐明。先前的研究已经表明嗅觉SCA2赤字,弗里德希氏共济失调和共济失调小群体的多样化的病因。设计/方法:之前验证翻译的16项气味鉴别试验从Sniffin棒(SS-16)是用来评估嗅觉36个常染色体显性共济失调(ADCA), 31个未知共济失调患者并与组的106名帕金森病(PD)患者和218名健康对照组。结果:所有392例证明SS-16共济失调的得分显著低于对照组(p < 0.001, 95%置信区间为β= 0.55 - 1.90)和共济失调的显著高于PD (p < 0.001, 95%置信区间为β= -4.58 - -3.00)当调整年龄(p = 0.001, 95% ci为β= -0.05 - -0.01),性别(p = 0.19)和吸烟史(p = 0.41)。结论:气味识别共济失调患者减少,但不要在特发性帕金森病一样的程度,进一步的研究是必要的确认中嗅觉减退的存在纯粹的小脑性共济失调。披露:Moscovich博士没有披露。穆尼奥斯博士没有披露。Teive博士没有披露。拉斯金博士没有披露。刘博士没有披露。麦克法兰博士没有披露。 Dr. Ashizawa has nothing to disclose. Dr. Lees has received personal compensation for activities with Genus, Novartis, Teva, Meda, Boehringer Ingelheim, GlaxoSmithKline, Ipsen, Lundbeck, Allergan, Orion, BIAL, Noscira and Roche. Dr. Lees has received research support from the PSP Association and Weston Trust - The Reta Lila Howard Foundation. Dr. Silveira-Moriyama has nothing to disclose.Wednesday, April 25 2012, 14:00 pm-19:00 pm