TY -的T1 -扩散磁共振成像异常长时间发热性癫痫发作后脑病JF -神经学乔-神经病学SP - 1304 LP - 1309做wnl.0000210487.36667 10.1212/01.。首页a5六世- 66 - 9 AU - j . Takanashi AU - h . Oba AU - a . j . Barkovich AU - h . Tada盟y田边AU - h .我去地狱谷野生猴园盟- s藤盟- m .加藤AU - m . Kawatani AU - a Sudo盟- h .小泽AU - t . Okanishi AU - m . Ishitobi AU - y Maegaki AU - y Koyasu Y1 - 2006/05/09 UR - //www.ez-admanager.com/content/66/9/1304.abstra首页ct N2 -背景:长期发作性脑病患者宣称最初症状通常在diffusion-weighted皮层下白质异常MRI(驾车)。目的:确定这些患者分享其他常见功能。方法:患者脑病预示长期癫痫发作和随后的皮层下白质异常识别MRI回顾性收集。综述了临床、实验室和放射数据。结果:17例,年龄在10个月到4年。都有长期发热性癫痫(超过1小时12例)作为他们的初始症状。随后的癫痫发作,常常成群的复杂部分发作,被认为首次发作后4到6天在16个病人。结果从正常到重度精神发育迟滞。MRI表现的2天内报告显示没有异常。 Subcortical white matter lesions were observed on DWI between 3 and 9 days in all 17 patients. T2-weighted images showed linear high intensity of subcortical U fibers in 13 patients. The lesions were predominantly frontal or frontoparietal in location with sparing of the perirolandic region. The diffusion abnormality disappeared between days 9 and 25, and cerebral atrophy was detected later than 2 weeks. Three patients having only frontal lesions had relatively good clinical outcome. Conclusions: Although the pathophysiologic mechanism remains unknown, these patients seem to have a distinctive encephalopathy syndrome. MRI is helpful in establishing the diagnosis of this encephalopathy. ER -