TY -的T1 -后quadrantic发育不良或hemi-hemimegalencephaly JF -神经学乔-神经病学SP - 2214 LP - 2首页220 - 10.1212/01. wnl.0000130459.91445.91六世62 - 12盟——m·D·达盟——a·巴斯托斯盟- c .水虎鱼盟a; 8:32 AU - t . Grisar盟诉总提苏尔AU - j·沙锥鸟盟- c . Juhasz AU - h·丘加尼AU - r . Guerrini AU - h .十字盟- e . Andermann盟a - f . Dubeau AU - j·蒙特斯AU - Olivier AU - f . Andermann Y1 - 2004/06/22 UR - //www.ez-admanager.com/content/62/12/2214.abstract N2 -介绍:后quadrantic发育不良(PQD),发育畸形涉及颞顶叶、枕叶和一个大脑半球,导致难治性癫痫。目的:描述19 PQD患者的临床特征和分析那些接受切除手术后的结果的发育异常的组织。方法:畸形的程度和性质主要是与高分辨率的脑成像评估。14个病人进行完全或部分temporoparieto-occipital切除或颞叶切除术与parieto-occipital断开联系在一起。术后随访期间从8个月到7年不等。作者恩格尔分类用于术后结果。结果:所有病人都是零星的。临床特点包括婴儿痉挛症,部分癫痫发作,精神发育迟滞,轻度偏瘫,视野缺陷。神经影像局部后大脑象限内的畸形侧的神经功能缺陷,并演示了hemi-hemimegalencephaly 14 5 19病人和multilobar皮质发育不良的19个病人。作者观察到的课堂我在六名病人的结果。 Two patients had class II and four patients had class III outcome. Class IV outcome was seen in two patients. After surgery, two patients developed mild hemiparesis, and two developed a visual field defect. Conclusions: Widespread cortical dysplasia is more frequent in the posterior quadrant. In our series, posterior quadrantic dysplasia represents either hemi-hemimegalencephaly or multilobar cortical dysplasia. Individuals with posterior quadrantic dysplasia share a spectrum of clinical features. The intractable epilepsy in these patients may be alleviated by a large quadrantic temporoparieto-occipital resection. ER -