TY -的T1神经疾病呈现Psuedotumoral脑干质量:一个案例报告JF -神经学乔-神经病学SP - S33 LP - S33做wnl.0000903288.32799 10.1212/01.。首页e2六世- 99 - 23补充2非盟-希瑟永盟-卡洛斯Camara-Lemarroy AU -卡塔洋Alikhani Y1 - 2022/12/05 UR - //www.ez-admanager.com/content/99/23_Supplement_2/S首页33.2.abstract N2 -目标,我们提出一个罕见的和神经疾病的诊断上具有挑战性的情况下(NBD)展现作为psuedotumoral脑干质量。背景Psuedotumoral-NBD遗传病的神经系统表现的疾病是罕见的。成像的特点是似的质量病灶增强对比度,hyperintense t2加权和fluid-attenuated反转恢复(天赋)和显示限制扩散。微分包含胶质病变,淋巴瘤,传染病和肉芽肿病变。设计/方法这是一个案例研究的33岁男性西非裔遗传病疾病的历史。结果33岁男性西非裔遗传病疾病的历史,提出两年后他的诊断头痛、低烧、生殖器溃疡,和水平的双眼复视。成像显示一个大右侧T2 /天赋hyperintense异常的髓质坏死的中心区域。脑脊液显示lymphocytic-predominant脑脊液细胞增多与11·106细胞/ L(参考范围0 - 5)和白细胞介素- 6的高水平。他的血管炎、传染性、多种、流式细胞术、自体免疫面板是负的。乙型肝炎核心抗原阳性,潜在的结核病。 The etiology for his presentation was believed to be parenchymal NBD and he received a 3-day course of intravenous solumedrol (eventually transitioned to prednisone and azathioprine) with significant improvement. Imaging 1-week post-treatment revealed resolution of enhancement, and at 3 months he had near complete lesion resolution.Conclusions NBD can rarely present with a psuedotumoral presentation, which can cause diagnostic uncertainty. A thorough radiologic/laboratory workup should be conducted to exclude other neurologic diagnoses; however, a high index of suspicion for NBD is required in similar cases and a spectacular response to steroids are invaluable in diagnosis. ER -