TY - T1的身体质量指数之间的联系和残疾儿童神经病学疾病摩根富林明腓骨肌萎缩——乔-神经病学SP - e1727 LP - - 10.1212 / WNL e1736做。首页0000000000012725六世- 97 - 17盟-加布里埃尔·a·Donlevy盟——莎拉·p·加内特盟凯拉医学博士科内特AU - Marnee j·麦凯盟詹妮弗·n·鲍德温AU -迷迭香r .害羞盟塞布丽娜w . Yum AU -盖Estilow盟伊莎贝拉莫洛尼非盟-玛丽亚Foscan盟Emanuela Pagliano AU -大卫。Pareyson盟马蒂尔德罗拉盟Trupti班达里AU -弗朗西斯科·Muntoni盟-玛丽·m·赖利AU -理查德·s·芬克尔AU -珍妮特·e·Sowden盟凯蒂·j·Eichinger盟Michael e .害羞-大卫·n·赫尔曼盟盟-伯恩斯盟约书亚Manoj p·塞斯Y1 - 2021/10/26 UR - //www.ez-admanager.com/content/97/17/e1727.abstract N2 -本研究背景和目标检查身体质量指数(BMI)之间的联系和残疾儿童与疾病腓骨肌萎缩(CMT)。首页方法我们进行了一项横断面分析477名患者CMT 3 - 20岁继承神经病财团和316岁——sex-matched健康儿童1000规范的项目。BMI是分类根据国际肥胖工作组(IOTF)标准,分类和BMI与健康的孩子。IOTF类别(成人等效切点)体重严重不足(BMI & lt; 17 kg / m2)、体重(体重指数≥17 & lt; 18.5 kg / m2),健康的体重(体重指数≥18.5 & lt; 25 kg / m2),超重(体重指数≥25 & lt; 30 kg / m2),和肥胖(BMI≥30 kg / m2)。分数在0到44-point CMT儿科规模(CMTPedS),经测量的残疾,检查在与体重指数的关系。结果有一个更高比例的CMT归类为儿童体重严重不足(5.7% vs 0.3%),体重不足(10.3% vs 5.1%),和肥胖(7.3% vs 3.8%) (p & lt;0.05)。更少的孩子与CMT归类为健康的体重(61.8% vs 74.4%) (p & lt;0.05),超重的比例(14.9% vs 16.5%)团体之间是相似的。CMTPedS分数(平均数±标准差)体重类别如下:体重严重不足27±9,体重不足20±8,健康的体重17±9,和肥胖超重17±9日22±10。 Compared to children with a healthy weight with CMT, being severely underweight was associated with being more disabled (p < 0.001), as was being obese (p = 0.015).Discussion The proportion of children with CMT who are underweight or obese is higher compared to age- and sex-matched healthy children. In children with CMT, being underweight or obese is associated with greater disability, when compared to children with CMT of healthy weight.BMI=body mass index; CDC=Centers for Disease Control and Prevention; CMT=Charcot-Marie-Tooth disease; CMTPedS=CMT Pediatric Scale; IOTF=International Obesity Task Force; 9-HPT=Nine-Hole Peg Test; 6MWT=6-minute walk test; WHO=World Health Organization; Nine-Hole Peg Test (9-HPT) ER -