TY - T1的成像评价丛状神经纤维瘤病1型摩根富林明纤维瘤——神经学乔-神经病学SP - S111 LP - - 10.1212 / WNL S119做。首页188金宝慱官网下载0000000000012437六世- 97 - 7补充1 AU - Shivani Ahlawat AU - k在Ly盟劳拉·m·法盟-迈克尔·j·费雪盟安德烈斯·j·莱辛盟——戴尔·j·伯格AU -约翰内斯·m·萨拉蒙盟盟Victor-Felix莫那Dusica Babovic-Vuksanovic AU - Eva Dombi盟戈登·哈里斯AU -斯科特·r·普罗金盟Jaishri布莱克利正在盟国际合作——代表缰绳Y1 - 2021/08/17 UR - //www.ez-admanager.com/content/97/7_Supplement_1/S111.abstract N2 -客观评估成像利用实践临床专家评估神经纤维瘤病1型(NF1)有症状和无症状的儿童和成人有或没有丛状纤维瘤(PN)。首页188金宝慱官网下载方法的一个管理机构审查board-exempt调查医护人员照顾患者NF1响应评价神经纤维瘤和Schwannomatosis(缰绳)会议2019年9月。调查的内容包括被调查者人口数据(9)的问题,类型的成像获得无症状的问题(4)和(4)问题症状的人没有PN,利用diffusion-weighted成像(2)的问题。结果30从业人员参与了调查。大多数学术神经肿瘤学在大容量(在10例/周)NF1中心。30人,26日访问全身MRI (WB-MRI)。最常见的方法一个无症状的人没有PN是成像(成人:57% (17/30);孩子们:50%(15/30)),其次是筛查WB-MRI(成人:20% (6/30);孩子们:26.7% (8/30))。最常见的方法有症状的人或已知PN地区核磁共振(成人:90% (27/30);孩子们:93%(28/30)),其次是WB-MRI(成人:20% (6/30); children: 36.7% [11/30]). WB-MRI was most often obtained to evaluate a symptomatic child with PN (37% [11/30]).Conclusions More than 90% of practitioners indicated they would obtain a regional MRI in a symptomatic patient without known or visible PN. Otherwise, there was little consensus on imaging practices. Given the high prevalence of PN and risk of malignant conversion in this patient population, there is a need to define imaging-based guidelines for optimal clinical care and the design of future clinical trials.ADC=apparent diffusion coefficient; DWI=diffusion-weighted imaging; MPNST=malignant peripheral nerve sheath tumor; NF1=neurofibromatosis type 1; PN=plexiform neurofibroma; PNST=peripheral nerve sheath tumor; REiNS=Response Evaluation in Neurofibromatosis and Schwannomatosis; STIR=short tau inversion recovery; SUV=standard uptake value; WB-MRI=whole-body MRI ER -