% 0期刊文章% Shivani Ahlawat % k在Ly %劳拉·m·法耶%安德烈斯·j·莱辛迈克尔·j·费舍尔% %戴尔·j·伯格%一个约翰内斯·m·萨拉蒙% % Victor-Felix莫那Dusica Babovic-Vuksanovic % Eva Dombi %一个戈登·哈里斯%斯科特·R·普罗金% Jaishri布莱克利正在%缰绳国际合作的代表% T的丛状纤维瘤成像评价神经纤维瘤类型1% B % D 2021% R 10.1212 / WNL调查评估。0000000000012437 % J首页神经病学% P S111188金宝慱官网下载-S119 % V 97% N 7补充1% X客观评估成像利用实践临床专家1型神经纤维瘤病(NF1)有症状和无症状的儿童和成人的评价有或没有丛状纤维瘤(PN)。方法的一个管理机构审查board-exempt调查医护人员照顾患者NF1响应评价神经纤维瘤和Schwannomatosis(缰绳)会议2019年9月。调查的内容包括被调查者人口数据(9)的问题,类型的成像获得无症状的问题(4)和(4)问题症状的人没有PN,利用diffusion-weighted成像(2)的问题。结果30从业人员参与了调查。大多数学术神经肿瘤学在大容量(> 10位病人/周)NF1中心。30人,26日访问全身MRI (WB-MRI)。最常见的方法一个无症状的人没有PN是成像(成人:57% (17/30);孩子们:50%(15/30)),其次是筛查WB-MRI(成人:20% (6/30);孩子们:26.7% (8/30))。最常见的方法有症状的人或已知PN地区核磁共振(成人:90% (27/30);孩子们:93%(28/30)),其次是WB-MRI(成人:20% (6/30);孩子们:36.7% (11/30))。 WB-MRI was most often obtained to evaluate a symptomatic child with PN (37% [11/30]).Conclusions More than 90% of practitioners indicated they would obtain a regional MRI in a symptomatic patient without known or visible PN. Otherwise, there was little consensus on imaging practices. Given the high prevalence of PN and risk of malignant conversion in this patient population, there is a need to define imaging-based guidelines for optimal clinical care and the design of future clinical trials.ADC=apparent diffusion coefficient; DWI=diffusion-weighted imaging; MPNST=malignant peripheral nerve sheath tumor; NF1=neurofibromatosis type 1; PN=plexiform neurofibroma; PNST=peripheral nerve sheath tumor; REiNS=Response Evaluation in Neurofibromatosis and Schwannomatosis; STIR=short tau inversion recovery; SUV=standard uptake value; WB-MRI=whole-body MRI %U //www.ez-admanager.com/content/neurology/97/7_Supplement_1/S111.full.pdf