@article {AhlawatS188金宝慱官网下载111作者= {Shivani Ahlawat和k在Ly和劳拉m法和迈克尔·j·费舍尔和Andr {\ ' e} s j·莱辛戴尔·j·伯格和约翰内斯·m .班子Victor-Felix莫那和Dusica Babovic-Vuksanovic和伊娃Dombi戈登·哈里斯和斯科特·r·普罗金Jaishri布莱克利正在和国际协作},代表缰绳title ={成像评价丛状神经纤维瘤病1型的纤维瘤},体积={97}={7补充1},页面= {S111——S119} = {2021}, doi = {10.1212 / WNL。出版商0000000000012437}= {Wolters Kluwer健康,公司代表美国神经病学学会},文摘={目的评估成像利用实践临床专家评估神经纤维瘤病1型(NF1)有症状和无症状的儿童首页和成人有或没有丛状纤维瘤(PN)。方法制度审查委员会{\ textendash}免除调查管理医疗从业者照顾患者NF1响应评价神经纤维瘤和Schwannomatosis(缰绳)会议2019年9月。调查的内容包括被调查者人口数据(9)的问题,类型的成像获得无症状的问题(4)和(4)问题症状的人没有PN,利用diffusion-weighted成像(2)的问题。结果30从业人员参与了调查。大多数学术神经肿瘤学在大容量(\ > 10位病人/周)NF1中心。30人,26日访问全身MRI (WB-MRI)。最常见的方法一个无症状的人没有PN是成像(成人:57 \ % (17/30);孩子们:50 \ %[15/30]),其次是筛查WB-MRI(成人:20 \ % (6/30);儿童:26.7 \ % [8/30])。最常见的方法有症状的人或已知PN地区核磁共振(成人:90 \ % (27/30);孩子们:93 \ %[28/30]),其次是WB-MRI(成人:20 \ % (6/30);儿童:36.7 \ % [11/30])。 WB-MRI was most often obtained to evaluate a symptomatic child with PN (37\% [11/30]).Conclusions More than 90\% of practitioners indicated they would obtain a regional MRI in a symptomatic patient without known or visible PN. Otherwise, there was little consensus on imaging practices. Given the high prevalence of PN and risk of malignant conversion in this patient population, there is a need to define imaging-based guidelines for optimal clinical care and the design of future clinical trials.ADC=apparent diffusion coefficient; DWI=diffusion-weighted imaging; MPNST=malignant peripheral nerve sheath tumor; NF1=neurofibromatosis type 1; PN=plexiform neurofibroma; PNST=peripheral nerve sheath tumor; REiNS=Response Evaluation in Neurofibromatosis and Schwannomatosis; STIR=short tau inversion recovery; SUV=standard uptake value; WB-MRI=whole-body MRI}, issn = {0028-3878}, URL = {//www.ez-admanager.com/content/97/7_Supplement_1/S111}, eprint = {//www.ez-admanager.com/content/97/7_Supplement_1/S111.full.pdf}, journal = {Neurology} }