TY - T1的神经性震颤继发于慢性免疫脱髓鞘与健壮的反应多神经病,静脉注射免疫球蛋白(P6.340) JF -神经学乔-神经学六世- 90 - 15补充SP - P6.340 AU - C昌西长矛AU -克里斯托弗·w·赫斯盟迈克尔·s·奥肯盟- William j .组织炎盟莱昂纳多阿尔梅达Y1 - 2018首页/04/10 UR - //www.ez-admanager.com/content/90/15_Supplement/P6.340.abstract N2 -目的:描述一个独特的运动障碍及其临床治疗反应。背景:神经性震颤(NT)是一种运动障碍的典型地震发生在孤立的周围神经病变。其现象学由一个姿势和/或动力地震影响远上肢与典型的频率范围在3到6赫兹之间。机制NT不是特点和病因广泛,但并没有明显的神经病变和震颤严重程度之间的关系。据估计,58%的病人患有慢性炎性脱髓鞘多神经病(CIDP)经历地震,导致更大的障碍。NT响应治疗潜在的神经病变在只有少量的情况下。设计/方法:视频案例报告。结果:57岁,右撇子的女人提出了进一步评估地震CIDP的上下文中。她神经病变之前十年的震动和体现进步的感觉和运动赤字和感觉性共济失调。为脱髓鞘神经传导研究引人注目的感觉运动多神经病与血清研究识别高葡萄糖浓度的硫酸化paragloboside (SGPG)抗体。地震影响了双边双手postural-kinetic为主,导致残疾的时候吃,喝和写作。她考试的其余部分与神经病变是相一致的。 She had a robust, early response to treatment with intravenous immune globulin (IVIg) with waning of effect towards the end of each six-week cycle. She was also taking propranolol and primidone daily and this was unchanged during treatment.Conclusions: We report a case of NT secondary to CIDP that had a robust response to treatment with IVIg. Response to treatment for neuropathic tremor is variable and better predictors of response to IVIg will need to be identified. The case and potential response predictors will be discussed.Disclosure: Dr. Spears has nothing to disclose. Dr. Hess has nothing to disclose. Dr. Okun has received personal compensation for consulting, serving on a scientific advisory board, speaking, or other activities with National Parkinson Foundation, Medscape, Mededicus. Dr. Triggs has nothing to disclose. Dr. Almeida has nothing to disclose. ER -